PGAM2 Mouse Monoclonal Antibody [Clone ID: LBI2F5]-抗体-抗体-生物在线
安诺伦(北京)生物科技有限公司
PGAM2 Mouse Monoclonal Antibody [Clone ID: LBI2F5]

PGAM2 Mouse Monoclonal Antibody [Clone ID: LBI2F5]

商家询价

产品名称: PGAM2 Mouse Monoclonal Antibody [Clone ID: LBI2F5]

英文名称: PGAM2 Mouse Monoclonal Antibody [Clone ID: LBI2F5]

产品编号: AMM11679V

产品价格: null

产品产地: 美国

品牌商标: Leading Biology

更新时间: null

使用范围: WB 1:500~2000, IF 1:50~100

安诺伦(北京)生物科技有限公司
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别名:GSD10; PGAM-M; PGAMM

产品概述:PGAM2 mouse monoclonal antibody, clone LBI2F5

总结:Phosphoglycerate mutase (PGAM) catalyzes the reversible reaction of 3-phosphoglycerate (3-PGA) to 2-phosphoglycerate (2-PGA) in the glycolytic pathway. The PGAM is a dimeric enzyme containing, in different tissues, different proportions of a slow-migrating muscle (MM) isozyme, a fast-migrating brain (BB) isozyme, and a hybrid form (MB). This gene encodes muscle-specific PGAM subunit. Mutations in this gene cause muscle phosphoglycerate mutase eficiency, also known as glycogen storage disease X. [provided by RefSeq]