FXN (Center) Peptide
产品名称: FXN (Center) Peptide
英文名称: FXN (Center) Peptide
产品编号: P2055
产品价格: 0
产品产地: 台湾
品牌商标: Abnova
更新时间: null
使用范围: null
亚诺法生技股份有限公司(Abnova)
- 联系人 :
- 地址 : 台湾台北市内湖区洲子街 108 号 9 楼
- 邮编 : 11493
- 所在区域 : 台湾
- 电话 : +886-920**1152 点击查看
- 传真 : 点击查看
- 邮箱 : sales@abnova.com.tw
- Specification
- Product Description:
- Rabbit polyclonal antibody raised against synthetic peptide of FXN.
- Immunogen:
- A synthetic peptide (conjugated with KLH) corresponding to internal region of human FXN.
- Host:
- Rabbit
- Reactivity:
- Human
- Form:
- Liquid
- Purification:
- Protein A purification
- Storage Buffer:
- In PBS (0.09% sodium azide)
- Storage Instruction:
- Store at 4°C. For long term storage store at -20°C.
Aliquot to avoid repeated freezing and thawing.
- Recommend Usage:
- ELISA (1:1000)
Western Blot (1:50-100)
Immunohistochemistry (1:50)
The optimal working dilution should be determined by the end user.
- Note:
- This product contains sodium azide: a POISONOUS AND HAZARDOUS SUBSTANCE which should be handled by trained staff only.
- Applications
- Western Blot (Cell lysate)
- Western blot analysis of CEM cell lysate (35 ug/lane) with FXN polyclonal antibody (Cat # PAB2011).
- Immunohistochemistry (Formalin/PFA-fixed paraffin-embedded sections)
- Formalin-fixed and paraffin-embedded human colon carcinoma tissue reacted with FXN polyclonal antibody (Cat # PAB2011) , which was peroxidase-conjugated to the secondary antibody, followed by DAB staining.
This data demonstrates the use of this antibody for immunohistochemistry ; clinical relevance has not been evaluated.
- Entrez GeneID:
- 2395
- Protein Accession#:
- NP_000135;Q16595
- Gene Name:
- FXN
- Gene Alias:
- CyaY,FA,FARR,FRDA,MGC57199,X25
- Gene Description:
- frataxin
- Gene Ontology:
- Hyperlink
- Gene Summary:
- This nuclear gene encodes a mitochondrial protein which belongs to FRATAXIN family. The protein functions in regulating mitochondrial iron transport and respiration. The expansion of intronic trinucleotide repeat GAA results in Friedreich ataxia. Alternative splicing results in multiple transcript variants. [provided by RefSeq
- Other Designations:
- OTTHUMP00000021428
- Related Disease
- Cardiomegaly
- Cardiomyopathies
- Cardiovascular Diseases
- Cerebellar Ataxia
- Chronic Disease
- Diabetes Mellitus, Type 2
- Disease Progression
- Edema
- Fragile X Syndrome
- Fragile X syndrome
- Friedreich Ataxia
- Friedreich's ataxia
- Genetic Predisposition to Disease
- Glucose Intolerance
- Interview, Psychological
- Muscular Atrophy, Spinal
- Myocardial Infarction
- Myotonic Dystrophy
- Myotonic dystrophy